28 April 2011

Septooptic Dysplasia

Coronal T2 showing absent septum pellucidum with characteristic configuration of frontal horns. Also note very thin optic chiasm (arrows). Thin corpus callosum and low fornices. Optic nerves are hypoplastic (not shown). Pituitary has normal appearance in this case. This is a case of Septooptic Dysplasia that is also known as De Morsier Syndrome.